Transition to KPL-387 Monotherapy Dosing & Administration Study

Purpose

The primary objective of this study is to characterize the efficacy and safety of dosing regimens used to transition from prior pericarditis therapies to KPL-387 monotherapy in participants with well-controlled recurrent pericarditis on standard therapies.

Conditions

  • Recurrent Pericarditis
  • Heart Diseases
  • Pericarditis

Eligibility

Eligible Ages
Between 18 Years and 80 Years
Eligible Sex
All
Accepts Healthy Volunteers
No

Inclusion Criteria

  • Has well-controlled recurrent pericarditis (i.e., including having CRP < 0.5 mg/dL within 14 days of Baseline and a pericarditis pain NRS score ≤ 3 at Baseline) - Has a documented history of CRP elevation (> 1 mg/dL) associated with at least one prior acute pericarditis episode, whether the incident event or any pericarditis recurrence - Has received treatment for RP for at least 3 months prior to Baseline with standard therapy(ies) and is currently on a stable dosing regimen including NSAIDs and/or colchicine, and/or glucocorticoids or an IL-1 pathway inhibitor (anakinra or rilonacept).

Exclusion Criteria

  • Has a diagnosis of pericarditis that is secondary to specific prohibited etiologies - Has had a pericarditis recurrence in the last 3 months prior to Baseline - Has received an investigational drug during the 4 weeks before study drug administration or is planning to receive an investigational drug at any time during the study. - Has a history of active or untreated, latent tuberculosis (TB) prior to screening. - Has a history of immunodeficiency. - Has a history of immunosuppression, including positive human immunodeficiency virus (HIV) test results. - Has chest x-ray at Screening or within 12 weeks before first study drug administration, with evidence of malignancy, abnormality consistent with prior or active TB infection or active infection. - Has a history of malignancy of any organ system within the past 5 years before Screening (other than a successfully treated non-metastatic cutaneous squamous cell carcinoma or basal cell carcinoma and/or localized carcinoma in situ of the cervix). - Has a known or suspected current active infection or a history of chronic or recurrent infectious disease (> 3 episodes in prior 12 months), including but not limited to, genitourinary infection, chest infection, sinusitis, or skin/soft tissue infection. - Has had a serious infection, has been admitted to the hospital for an infection, or has been treated for a documented infection requiring antibiotics for a documented infection within 2 weeks prior to first study drug administration. - Has had an organ transplant (except corneal transplant performed more than 3 months prior to first study drug administration). - In the Investigator's opinion, has any other medical condition that could adversely affect the subject's participation or interfere with study evaluations.

Study Design

Phase
Phase 2
Study Type
Interventional
Allocation
Non-Randomized
Intervention Model
Single Group Assignment
Primary Purpose
Treatment
Masking
None (Open Label)

Arm Groups

ArmDescriptionAssigned Intervention
Experimental
Posology KPL-387
In Posology Study, KPL-387 will be administered by subcutaneous (SC) injection through Week 16.
  • Drug: KPL-387
    administered by subcutaneous injection
Experimental
Long-Term Extension
Participants from Posology Study who continue into the Long-Term Extension will receive KPL-387 for up to 24 months or until KPL-387 is approved for commercial use in that region to treat pericarditis, whichever occurs first.
  • Drug: KPL-387
    administered by subcutaneous injection

Recruiting Locations

Investigational Site 031
Phoenix, Arizona 85054

Investigational Site 014
Los Angeles, California 90048

Investigational Site 002
Santa Monica, California 90404

Investigational Site 013
Chicago, Illinois 60611

Investigational Site 025
Baltimore, Maryland 21287

Investigational Site 028
Rochester, Minnesota 55905

Investigational Site 011
New York, New York 10016

Investigational Site 003
New York, New York 10032

Investigational Site 009
Cincinnati, Ohio 45219

Investigational Site 005
Austin, Texas 78705

Investigational Site 006
Houston, Texas 77030

Investigational Site 004
Charlottesville, Virginia 22903

Investigational Site 001
Norfolk, Virginia 23507

Investigational Site 008
Richmond, Virginia 23284

More Details

Status
Recruiting
Sponsor
Kiniksa Pharmaceuticals International, plc

Study Contact

Clinical Project Manager
781-431-9100
clinicaltrials@kiniksa.com

Detailed Description

During the Posology (Dosing and Administration) Study, participants on oral pericarditis therapies alone (i.e., non-steroidal anti-inflammatory drugs [NSAIDs], colchicine, and/or glucocorticoids) and participants on Interleukin-1 (IL-1) pathway inhibition drugs will transition to KPL-387 per protocol guidelines. Participants will receive KPL-387 for up to 16 weeks in the Posology Study. At study visits throughout the Posology Study, participants will be queried for symptoms of chest pain (and participants will fill out pericarditis pain numerical rating scale [NRS] scores) and will be assessed for physical signs (e.g., pericardial friction rub) and laboratory evidence of pericarditis activity (e.g., C-reactive protein [CRP]) as well as treatment tolerability and pharmacokinetics (PK). Participants experiencing new or worsening symptoms consistent with pericarditis will be managed per study protocol. All active, enrolled participants in the Posology Study who have not completed an End of Treatment (EOT) Visit may be eligible to transition into the Long-Term Extension (LTE) following completion of the Week 16 Visit. The Week 16 Visit will serve as both a Posology Study End of Study Visit and a Baseline Visit for the LTE. Participants who choose not to participate in the LTE will complete an EOT Visit followed by a Safety Follow-Up until 8 weeks after the last KPL-387 dose administration. The open-label LTE is designed to evaluate the long-term efficacy and safety of KPL-387 in recurrent pericarditis (RP). Treatment in the LTE may continue until the participant has received up to 24 months of treatment in the LTE or until KPL-387 is approved for commercial use in that region to treat pericarditis, whichever occurs first. At study visits throughout the LTE, participants will be queried for symptoms of chest pain (and participants will fill out pericarditis pain NRS scores) and will be assessed for physical signs (e.g., pericardial friction rub) and laboratory evidence of pericarditis activity (e.g., CRP) as well as treatment tolerability and PK. Participants experiencing new or worsening symptoms consistent with pericarditis will be managed as described in the protocol.